ESPGHAN - Monothematic Conference on The Gastrointestinal, Hepatologic and Nutritional Aspects of Cystic Fibrosis

Thursday 4 April

Coordinators: Carmen Ribes-Koninckx, Frank Bodewes and Michael Wilschanski

  • 13:00-14:15 Arrival, registration and lunch
  • 14:15 Welcome (Carmen Ribes-Koninckx)

14:30 – 16:00 SESSION 1: GENERAL ASPECTS Update

Chair: Carmen Ribes-Koninckx, Frank Bodewes

  • 14:30 CFTR update 2019: A special focus on GI pathology (Michael Wilschanski)
  • 15:00 CFTR mutations: impact on pancreatic function (Isabelle Scheers)
  • 15:30 New Born Screening: GI and Nutritional aspects. Consequences for early CFTR modulation treatments (Anne Munck)
  • 16:00 Coffee Break

16:15 – 18:15 SESSION 2: A CLINICAL VIEW

Chairs: Michael Wilschanski, Kris De Boeck

  • 16:15 CF Liver disease: from diagnosis to liver transplantation (Dominique Debray)
  • 16:45 Intestinal lipid absorption and bile salt regulation (Frank Bodewes)
  • 17:15 Dysmotility disorders in CF: much more than GERD (Etna Masip)
  • 17:45 Abdominal pain, differential diagnosis and management (Carla Colombo)

Friday 5 April

8:30- 9:30 SESSION 3: CLINICAL CASES

Chairs: Isabelle Scheers, Dominique Debray

  • Clinical cases presented by the delegates
  • Selected abstracts (total 6)

9:30 – 12:00 SESSION 4: NUTRITIONAL ASPECTS

Chairs: Anne Munck, Carla Colombo

  • 9:30 How to assess nutritional status? Anthropometry and biomarkers (Chris Smith)
  • 10:00 How to deal with malnutrition? (Jessie Hulst)
  • 10:30 Coffee Break
  • 11:00 Bone disease in cystic fibrosis: new pathogenic insights and novel therapies (Isabelle Sermet)
  • 11:30 CF-related glucose metabolism and impact on nutrition (Dimitri Declercq)
  • 12:00 Nutritional recommendations: Diet and PERT (Inês Asseiceira)
  • 12:30 Lunch

13:30 SESSION 5: NEW THERAPIES AND STRATEGIES

Chairs: Michael Wilschanski, Jessie Hulst

  • 13:30 New evidences and opportunities on PERT. MyCyFAPP H2020
    • 13:30-13-40 MyCyFAPP: Innovative approach for nutrition and PERT self-management in CF (Carmen Ribes)
    • 13:40-14:00 New evidence-based method to adjust PERT (Joaquim Calvo Lerma)
    • 14:00-14:15 Lessons learnt from MyCyFAPP clinical trial (Paula Crespo Escobar)
  • 14:15 Pancreas transplantation, does it have a place in CF treatment? (Frank Bodewes)
  • 14:45 Do CFTR modulator therapies improve GI outcomes? (Kris De Boeck)
  • 15:00 Stem cell-derived organoids to model gastrointestinal facets of cystic fibrosis and to evaluate new therapies outcomes (Karin de Winter)
  • 15:30 End of the course & Farewell

 

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